Endovascular stenting of chronic retrohepatic inferior vena cava interruption in Budd-Chiari syndrome.
Budd-Chiari syndrome is a rare cause of hepatic venous outflow obstruction, with heterogenous etiologies. We report the case of a 35-year-old man with chronic, compensated Budd-Chiari syndrome due to retrohepatic inferior vena cava (IVC) occlusion, likely resulting from early-life thrombosis. Imagin…
"Intrapericardial Approach" for Venous Outflow Reconstruction in Living-Donor Liver Transplantation for Budd-Chiari Syndrome: Surgical Techniques and LongTerm Outcomes.
Unlike deceased-donor liver transplantation, living-donor liver transplantation (LDLT) for Budd-Chiari Syndrome (BCS) presents distinctive challenges in hepatic venous (HV)-outflow reconstruction because diseased HV-inferior vena cava (IVC) cannot be entirely replaced with healthy donor vessels. In…
Not all acute peripheral facial palsy in children recovers completely: A telediagnostic follow-up study.
Up to 30% of adults with peripheral facial palsy (FP) develop synkinesis, but it's incidence in children remains unclear due to limited long-term data. Children (<18 years) treated for acute peripheral FP at Jena University Hospital between 2009 and 2021 were screened in this cross-sectional study.…
Budd-Chiari Syndrome Due to Protein C Deficiency: A Case Report.
Budd-Chiari Syndrome (BCS), a rare vascular disorder of the liver characterized by obstruction of hepatic venous outflow, has an estimated prevalence of approximately 1 in 100,000 in the general population. Among its various etiologies, coagulation factor deficiencies are uncommon. This case, follow…
Pregnancy After In Vitro Fertilization in Budd-Chiari Syndrome Secondary to Polycythemia Vera: Multidisciplinary Management and Perioperative Considerations.
Budd-Chiari syndrome (BCS) is a rare hepatic vascular disorder frequently associated with prothrombotic conditions such as myeloproliferative neoplasms. Pregnancy and assisted reproductive technologies further increase thrombotic and portal-hypertensive risk. We report a successful in vitro fertiliz…
Cervicomedullary CSF space obliteration as a risk factor of reoperation in Chiari malformation type I.
In patients with Chiari malformation type 1 (CM1), it is unclear whether severe cervicomedullary CSF space crowding on preoperative MRI is associated with postoperative outcomes. We tested whether a binary classification scheme of cervicomedullary CSF space crowding (obliteration vs. non-obliteratio…
Tectal thickening in pediatric population: Clinical correlates and association with hydrocephalus.
The tectal plate can be affected by a broad spectrum of pathological processes, resulting in diverse clinical manifestations. These include primary or metastatic tumors, granulomatous diseases, cerebrovascular malformations, ischemic insults, traumatic injury, lipomas, cysticercosis, and degenerativ…
Prenatal and Postnatal Ultrasound Findings of Congenital Diaphragmatic Hernia Associated With Myelomeningocele, Chiari II Malformation, and Renal Dysplasia.
Congenital diaphragmatic hernia (CDH) associated with neural tube defects is exceedingly rare. We report a female neonate (2550 g) born at 35 weeks (Apgar 2/4/5) with severe left-sided Bochdalek CDH, lumbosacral myelomeningocele, Chiari II malformation, and unilateral renal dysplasia.…